Adult hepatoblastoma: case report with adrenal recurrence.
نویسندگان
چکیده
Hepatoblastoma is the most frequent primary liver tumor of childhood, with an annual incidence of 0.5-1.5 cases per million (1). It is very rare in adults, with a controversial existent since some authors believe that most of them are really underdiagnosed hepatocarcinomas, mixed sarcomas or hepatic cholangio-hepatocarcinomas. To date, there are only 40 reported cases of hepatoblastoma in adult patients. The first case was described by Barnett in 1958. (2) The only available treatment that has improved survival is radical surgery (R0). The main difference with children is the frequency of lymphatic or hematogenous metastases, which are extremely rare in the pediatric population (3,4).
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ورودعنوان ژورنال:
- Revista espanola de enfermedades digestivas : organo oficial de la Sociedad Espanola de Patologia Digestiva
دوره 105 10 شماره
صفحات -
تاریخ انتشار 2013